eRAM
encyclopedia of Rare Disease Annotation for Precision Medicine
| Disease | amyloidosis |
| Comorbidity | C0027726|nephrotic syndrome |
| Sentences | 15 |
| PubMedID- 23314147 | Patients are at variable risks for the development of systemic reactive (aa) amyloidosis, leading to the nephrotic syndrome and kidney failure. |
| PubMedID- 21502717 | We report the case of a patient with renal amyloidosis associated with nephrotic syndrome who maintained remission for 6 years after undergoing high-dose chemotherapy followed by autologous peripheral blood stem-cell transplantation (auto-pbsct). |
| PubMedID- 20729743 | Despite this treatment, she developed secondary amyloidosis with nephrotic syndrome 4 years after the initial presentation. |
| PubMedID- 20091495 | We herein report a case of traps complicated with nephrotic syndrome due to aa amyloidosis in which treatment with etanercept was associated with remission of the nephrotic syndrome but no regression of amyloid mass on the follow-up renal biopsy. |
| PubMedID- 25984105 | A 46-year-old caucasian female, affected by nephrotic syndrome, was diagnosed with al amyloidosis by renal biopsy (figure 1), performed on the left kidney (maximal longitudinal renal axes 10.9 cm), in december 2006, with an igg-λ as monoclonal protein. |
| PubMedID- 23235953 | Rikitake et al., however, reported lambda light chain proteinuria in a 57-year-old female who developed fanconi syndrome and had renal amyloidosis with nephrotic syndrome for the last 5 years [132]. |
| PubMedID- 25579733 | The patients developed nephrotic syndrome due to secondary amyloidosis, which was refractory to the immunosuppressive agents. |
| PubMedID- 25984151 | We report a patient with sjia and nephrotic syndrome due to aa amyloidosis successfully treated with an anti-interleukin-6 receptor (anti-il-6r) antibody, tocilizumab. |
| PubMedID- 22760913 | In this case, chronic inflammation with abdominal and joint symptoms and nephrotic syndrome due to secondary amyloidosis in an arab patient raised the hypothesis of fmf, even in the setting of quick renal function decline. |
| PubMedID- 23472940 | Tocilizumab treatment for nephrotic syndrome due to amyloidosis in behcet's disease. |
| PubMedID- 24516769 | [4] other manifestations include, recurrent infections, hyperviscosity induced arterial infarctions and venous thrombosis, neurological impairment, nephrotic syndrome, extramedullary involvement of various organs, concomitant amyloidosis with gastrointestinal symptoms, and soft tissue or solitary bone masses (plasmacytomas). |
| PubMedID- 25984052 | But there is no case with nephrotic syndrome due to amyloidosis documented with renal biopsy. |
| PubMedID- 25969671 | One case report is about a child, who in addition to fmf had several prothrombotic defects [4], the second about a 21 year-old man with nephrotic syndrome complicated by aa amyloidosis, and lupus anticoagulant in low titre [5], the third about a young patient who suffered of a brain stem infarction during a typical fmf attack [6]. |
| PubMedID- 25572486 | Remission of nephrotic syndrome due to aa-amyloidosis, complicating familiar mediterranean fever, with tocilizumab. |
| PubMedID- 24558629 | Here, a case of biopsy-proven renal aa amyloidosis complicated with nephrotic syndrome associated with lung carcinoma is reported. |
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